18. Hydrocephalus in granulomatosis with polyangitis secondary to CNS vasculitis
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چکیده
منابع مشابه
Bronchoscopic Management of Tracheobronchial Stenosis Secondary to Granulomatosis with Polyangitis: A Case Report
Granulomatosis with Polyangitis (GPA), previously known as Wegener’s Granulomatosis, is a form of anti-neutrophil cytoplasmic antibodies (ANCA)-associated vascuilitis predominantly involving the upper and lower respiratory tract and kidneys. Tracheobronchial involvement in GPA can have varied manifestations which include airway inflammation, mucosal granulomas, tracheobronchial stenosis, trache...
متن کاملGranulomatosis with polyangitis presenting with multiple cranial nerve palsies
Case presentation We report the case of localised granulomatosis with polyangitis in a 27 year old Caucasian gentleman who presented with multiple cranial neuropathies. He reported diplopia, hearing loss, dysphagia and dysarthria due to involvement of VI, XIII, IX, X and XII cranial nerves. A cerebral MRI demonstrated pachymeningitis along with mastoid changes and additional diagnostic workup s...
متن کاملEosinophilic Granulomatosis with Polyangitis Presenting as Cardiac Tamponade.
Eosinophilic granulomatosis with polyangitis (EGPA; earlier called Churg-Strauss syndrome) is a small-vessel necrotising vasculitis typically characterised by asthma, lung infiltrates, extra-vascular necrotising granulomas and hyper-eosinophilia. Cardiac disease is a major contributor to disease-related deaths in EGPA. We describe the case of a 39-year-old woman with late onset asthma, allergic...
متن کاملFamilial vasculitides: granulomatosis with polyangitis and microscopic polyangitis in two brothers with differing anti-neutrophil cytoplasm antibody specificity
Anti-neutrophil cytoplasm antibody (ANCA)-associated vasculitis (AAV) is a group of rare autoimmune diseases. Although the aetiology of AAV is uncertain, it is likely that genetic and environmental factors contribute. We report the unusual case of two brothers presenting with AAV with differing clinical pictures and differing ANCA specificity. There is a recently identified difference in geneti...
متن کاملTotal Nasal Skeletal Reconstruction Disfigured by Granulomatosis with Polyangitis (Wegener Granulomatosis)
BACKGROUND Nasal deformity is a common disorder in Wegener granulomatosis, which is produced by polyangitis of medium-sized vessels. This process may cause necrosis and destruction of the nasal mucosa and osteocartilaginous framework. At this time, there is a lack of published data on nasal deformities associated with Wegener granulomatosis. METHODS We present a 53-year-old woman with complet...
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ژورنال
عنوان ژورنال: Rheumatology Advances in Practice
سال: 2017
ISSN: 2514-1775
DOI: 10.1093/rap/rkx010